ࡱ> RUQc R;bjbj8LMbMbB4 ;;;;;OOO8LDO- "999mT,-------$/}2@-!; mm  @-;;994a-{*{*{* | ;9;9-{* -{*{***9 e/(*-w-0-*2)2*2;*  {*     @-@-{*   -    2          Q : lf[b2020t^NGS,gՋuiryf[NN NNՋ'Y~ N0NN Tyuiryf[ N0NNNx071001 N0Ջvv hQb8hnfؚ!hNy(+TؚL)^J\kNu[uiryf[NNwƋvW,gi_0Stvcc z^S^(u gsQSt㉳Q[EvR0 V0ՋV NNՋS+TuirSf[T_uirf[$Nf[yvQ[ RpeT`S50%0 N0ՋW (N) T͋ʑ30R0 (N) b 40R0 ( N)$Re 20R0 (V){T{ 40R0 (N) 40R0 (mQ){ 30R0 mQ0Ջf^ [fv~`S30% -NI{^v~`S50% ^'Yv~`S20%0 D 0uirSf[ 00 0_uirf[ 0Ջ'Y~0 ,{NR 0uirSf[ 050% ,{Nz ~ 1ccuirSf[vi_TxvzQ[ 2q`uirSf[vxvzV 3NuirSf[SU\{S0 ,{Nz 8hxv~gNR N8hxvy{|TR^ 8hxvN,'`( 8hxvuirf[R RP[BgN q`8hxvSf[~b cc8hxvN~~g DNAvSe~g tRNAvN~~g 8hxv+}Y8T6e'`( 4Ƌ8hxvS'`0 Y'`0XrHe^0QrHe^0RP[BgN0Tm0Ve~gI{i_0 ,{ Nz ˆ}v(Sf[ 1Ƌ_(lWx0(lWxvI{5upPI 0.0(lWxkW0-e0bS0~gW0{USˆ}v(0 YTˆ}v(0vg0vn05ul0ˆ}v(vS'`N Y'`I{vi_ 2cc(lWxv~g_0ˆ}v(vN~~g0ˆ}v(vN~~g0ˆ}v(v$N'`5uy'`(SI{5up0S'`N Y'`vStS+}Y8T6ev'`(0ˆ}v(Ry~SvN,St 3q`ˆ}v(vؚ~~gNRvsQ| N(lWxvR{|0͑v)Y6q[0(lWxTˆ}v(vN,tS'`(0ˆ}v(vR{|Tˆ}v6RBRv^(u0 ,{Vz v 1ƋhQv0vv~TMOTPSMO0+RgHe^0 T]v0S'`b6RBR0 NS'`b6RBR0zN'`b6RBR0^zN'`b6RBR0s|l8^pe0vUSMO0k;mR0vvVEUSMOI{i_ 2ccvv\O(u:gt0v;mRvKm[0vvc~ 3q`vOS^RRf[ NvvR{|T}T T0 ,{Nz |vRN" 1Ƌ|u0Nnx1"lv|0 Nx_s0-n bNx1"lv|0xx b|_I{i_ 2cc|u㉌TTCA_svSf[S z0Sf[ϑSc0NnxvS 3q`|u0TCA_sTxx b|_vuirf[aIN0xx b|_vSf[S z 4NS|TY|vvOM0 ,{mQz uir'lSN'lSxxS 1Ƌuir'lS05uP[ O0^ir4ls^xxS0'lSxxS0x'lk0vPTBRI{i_ 2ccuir'lSvǏ zTe_05uP[ OvRN~b0'lSxxSN5uP[ OvvPT0~|SOvzh|~I{wƋ 3q`'lSxxSv:g6R0vPTTb6R\O(u 4NvQN+gz'lSv|~0 ,{Nz |vuirTb 1ƋIQS^0fS^0aS\e_s0C4_s0IQTxxS0|_uI{i_ 2cc|_uvSf[S zSsQ.vvc0|u㉌T|_uvNe 3q`|SvTbǏ z 4NIQv8T6e0lST TSRvNu0|TY|vuirTb0 ,{kQz {|N" 1ƋRXT0o }Oea'`vHSL 0-'lS0-'lS0-'lS0nSO0pW}SOˆ}v0Refsum s Disease+YςYluu 0kxzh|~0gjxlЏ|~0pW}SOˆ}vACP 0xTvFAS I{i_ 2ccvPpexSP[xv-'lSSf[S zTϑ{ 3q`xv-'lST-'lS_0YNx_s0xvN4YTbǏ z 4N㉨RirvmST8T6e0N"v0 NpulvuirTb0 ,{]Nz ˆ}v(vvOM㉌T(lWxvRNlS 1Ƌl }0(lWxN"^01(lW\O(u01W\O(u0l(lW\O(u0a| N(lx_s0?\ }_s0u|(lWx0un(lWx0Nn?\uPKU I{vsQi_ 2cc(lWxvRN"Ǐ z Q(lvegnN(lvS0(lvlЏ0-nxvN"lS 3Nߘir-Nˆ}v(vmS8T6e0~ހQˆ}v(M01u(lWxMuvvQNSTir0 ,{ASz (lv TST(lWxvuirTb 1Ƌ_(lWxessential amino acids 0NxUSMOvi_ 2cc(l2upxxvTb_07(lxvb_b_0Glnvb_b_ 3q`uirV.lvuirSf[0]xx؏S\O(u0IpYNxegnTS 4N.l }_s0(lWxuirTbvN,_0Te(lWxvTbSvNsQ|0 ,{ASNz 8hxvvOM㉌T8hxN" 1Ƌ8hxv0P6R'`QRv0uΘ0@gb6R\O(u0Lesch-Nyhan~Tu0sNnx?\uI{i_ 2cc VdTxT'VvUxvR0 VdT8h|8hxvTb0'VvU8h|8hxvTb01'l8h|8hxvTb 3N8hxvvOM0 ,{ASNz 8hxvuirTb 1ƋJSOYu Y6R0JS Nޏ~ Y6R0 Y6Rwp0KlenowGrk0MR[0nT0Q]Grk0APMO0lU_0 N[ylU_0/TRP[0PribnowvI{i_ 2ccDNAvuirTb0RNAvuirTb q`DNAvSlU_\O(u 3NDNAv_c$O0O YNzS08hxTbvb6RBR0WV] z0 ,{AS Nz ˆ}v(vuirTb 1Ƌ[xP[0W O[x0SD^R0_>eFhgORF 0RP[4OO0OSI{i_ 2 $8:HPXhtx $ : B D L Z j t   $ & > Ȳ|hhhh'hILh#CJOJPJQJ^JaJo(!h#CJOJPJQJ^JaJo('hILhILCJOJPJQJ^JaJo(!hILCJOJPJQJ^JaJo(*huhhIL5CJOJPJQJ^JaJo(h;5CJ$OJQJaJ$hIL5CJ$OJQJaJ$o(hu5CJ$OJQJaJ$h;5CJ$OJQJaJ$o($*:Rv $ n  0 R j  dgd#dgdIL 2dWD`2gduh$a$> D F H X j   ڰڟuaJ3J-huhhw5CJOJPJQJ\^JaJo(-huhh;5CJOJPJQJ\^JaJo('h#5CJOJPJQJ\^JaJo(*hILh#5CJ OJPJQJ\^JaJ'h#h;CJOJPJQJ^JaJo(!h#CJOJPJQJ^JaJo(*huhhIL5CJOJPJQJ^JaJo('hILh#CJOJPJQJ^JaJo('hILhILCJOJPJQJ^JaJo(!hwCJOJPJQJ^JaJo(        $ ( D L b j D F H L ppp]pppLppLpL!hW0CJOJPJQJ^JaJo($huh5CJOJPJQJ^JaJo('h+)h+)CJOJPJQJ^JaJo(!h+)CJOJPJQJ^JaJo(*huhhuh5CJOJPJQJ^JaJo(*huhh+)5CJOJPJQJ^JaJo(-huhh;5CJOJPJQJ\^JaJo($h5CJOJPJQJ\^JaJ'h5CJOJPJQJ\^JaJo( $ H f H L lxL $dha$gdy'$-dhWD`-a$gduh & F*dh@&WD`*gd4$-dh@&G$WD`-a$gduh *dhWD`*gd+) $-dh1$UD WDXD2YD2]`-a$gduh H P lx| HPz*2z x$,hpBJıĠ$h+)h+)CJOJPJQJ^JaJ!h=CCJOJPJQJ^JaJo($huh5CJOJPJQJ^JaJo(*huhh+)5CJOJPJQJ^JaJo(!hW0CJOJPJQJ^JaJo('h+)h+)CJOJPJQJ^JaJo(7Lz.~|(lF$-dh1$WD`-a$gduh$-dh@&G$WD`-a$gduh *dhWD`*gdW0$-dhWD`-a$gduh *dhWD`*gd+)FPn<b(B\8x*,^,~,,$-dh1$WD`-a$gduh$-dhWD`-a$gduh *dhWD`*gd+)8BLTnt,\jr<bf$,B\`4<x,&,.,òòòòòU$h+)h+)CJOJPJQJ^JaJ'h+)h+)CJOJPJQJ^JaJo(!h=CCJOJPJQJ^JaJo(*huhh+)5CJOJPJQJ^JaJo('huhh+)5CJOJPJQJ^JaJ$huh5CJOJPJQJ^JaJo(6ccˆ}v(Tb OW O[xyrpI{wƋ 3q`ˆ}v(vTbSO| Nˆ}v(vЏT[MO0 ,{ASVz ir(N"vT|Sc 1ƋMRTS0MRo;mNSb6R0[irS[v0;O\O(uS;Ov0~bvI{i_ 2q`|N"0N"0(lWxN"S N'Y{|ir(N"vT|Nc 3NN"vV~4ls^0 ,{NR 0_uirf[ 050% ,{Nz ~ 1.Ƌ_uiri_ 2.Rg_uirvqQ'` O_uir[N{|vq_T 3.ON{|[_uirNLuvƋvN*N6k f[`N_uirvNR0 ,{Nz S8h_uirvb_` g TR 1.ƋS8huir ~̃ <X~̃ Su(SO b[ Z k 4Ob[vfSO >e~̃ /eSSO cSSOTzKQ!klSOvi_ 2.O~̃vW,gg TR 3.RgG+TG-~̃~ހXv_ T 4.~TRgipQlgrlv:g6R0 ,{ Nz w8h_uirvb_` g TR 1.Ƌw8h_uir uk̃ ̃ GP̃N rTTv[IN 2.Ow̃0uk̃ṽSOyrp A~ke_ ~ހg SvQ~ހXv~g 3.Ov^RgT{| N Tuk̃vu;mSTT6kvyrp 4.Rgk~̃0>e~̃0uk̃T ̃~ހXbR0̃=v_ T NS[NSu(SO6RYel 5.Rgk ̃v%{Q̃NTlũNvyrp NS[NvyrS~g0 ,{Vz ukNNuk 1.Ƌuk wuk Nuk lṼe p'`lṼSO )nTlṼSO nS̃ nS'`[IN 2.Ouk|[ySOvy{| ky[yvyrkYb_vNhuk 3.Rgp'`lṼSOvˆ'`u;mSTNekuf~vyr_Spe0 ,{Nz _uirv%{QNW{QW 1.Ƌ{Q_uir _{Q_uir %{Q %{Qir C/N (lWx{QWuir (lWx_{QWuir uVP[ 'YϑCQ } _ϑCQ } W{QWv[IN 2.OV'Y{|_uirvgupHVS8^(uvW{QW Ty _uirvmQ'Y%{Q } 3.Y^(ut+R'`W{QW Ot+R'`W{QWvO(uvSt 4.RgW{QWvR{|elT^(uV0 ,{mQz _uirveHN" 1.ƋeHN" uir'lS g'l|T8T e'l|T8T Su 'lSxxS IQTxxS ^ir4ls^xxS N"eP_ SticklandS^v[IN 2.Ouir'lSvb__0Ǐ z0RS{|W NSS_{Q_uirvuir'lS-N 1"lTNv_ Rgv^kT_v;Nyrp OR }b6R̃:g6R 3.Rg g'l|T8T0e'l|T8T0Suv_ TpNS TWT_WsNxSu~v_ T 4.Ƌv^OuirV.lvvyr'`TV.lǏ z NS'YRP[ir(Z|TbvǏ z0 ,{Nz _uirvuSvQc6R 1.ƋUS~ހ_uirxQWuf~ gu)n^ ]lmkl bu } uP6RVP[ mp̃0mk0Su02P ޏ~W{Q R`SW{Q R`JmW{Q Sf[@g̃BR mkBRvv[IN 2.OxQWuf~vQ*NegTTgyrp 9hncTegvyrp Rg(WwQSOuN-Nv^(u 3.RgR`JmW{QTR`SW{Qv_ T NSmp̃0mk02PTSuv_ T 4.O_uiruA~kvKm[el ؚ)nmp̃vStTel bu }[_uirv\O(u:g6R0 ,{kQz _uirvW OS_Ty 1.ƋWVzS %{Q:wW IQ Y;m\O(u WV͑~ ~T lS l[ lg :wlṼSO p YX QQr^ql Q'`ukv[IN 2.O_uirW Oir(vyrp 6qLu_uirWV͑~ve_ (WW Oy-Nv^(u %{Q:wW_uirvyrp Rg%{Q:wW_uir(WwQSOuN[-Nv^(u 3.OAmes[hKmLvBRvtOnc v^[vQ(WsXvKmebRN)R(u 4.ÕypvSV Y[p̃*hۏL YX YۏLcknxṽyOυ0 ,{]Nz _uirvu` 1.Ƌ4lSOQ\O(u 'Ỹpe ck8^̃ _u`6RBR ẽRir Nu qQu [u bb m̃W{Q BOD COD ;m'`allv[IN 2.)R(u_uirN"yrp ۏLal4lYt0sXltv^(u0 ,{ASz OgNMQu 1. Ƌ^yr_'`MQuv~~~gNMQuv:g6RSyr_'`MQuvvsQwƋTMQu~ހ0bS0bSOvW,gi_ 2.NMQuf[elSvQ^(uvvsQQ[S;NbSOS^vN,ĉ_ Blcc NyS^{|WShb/g0 ,{ASNz _uirvR{|Tt[ Ƌ_uirvy0ey0̃*hv[IN OS}T Tl}T TSR0 SfNv [1] y,2018 [2] hT_^._uirf[Ye z(,{3Hr).SN:ؚI{YeQHr>y,2011     PAGE  PAGE \* MERGEFORMAT2 .,^,f,h,~,,,,,- -:-<-D-F-R-V-X-Z-ձ뱠yfyUBy$h5CJOJPJQJ^JaJo(!h5CJOJPJQJ^JaJ$h:75CJOJPJQJ^JaJo(*huhhy'5CJOJPJQJ^JaJo(!hE5CJOJPJQJ^JaJ!hCJOJPJQJ^JaJo(!h=CCJOJPJQJ^JaJo($huh5CJOJPJQJ^JaJo(*huhh+)5CJOJPJQJ^JaJo('h+)h+)CJOJPJQJ^JaJo(,-:-<-Z-h-~---...../P///(0j0001L1 $dha$gd%g *dhWD`*gdy' $dha$gdy' *dhWD`*gd+)Z-`-b-h----....../(0*0j00L1j1~2222&4(4p4r44&6F678888899ua'hy'h%gCJOJPJQJ^JaJo('h%gh%gCJOJPJQJ^JaJo($hy'hy'CJOJPJQJ^JaJ!h%gCJOJPJQJ^JaJo($huh5CJOJPJQJ^JaJo('hy'hy'CJOJPJQJ^JaJo(*huhhuh5CJOJPJQJ^JaJo(*huhhy'5CJOJPJQJ^JaJo(&L1j11D2~222J33&4r446555&6F66\7778888>99 *dhWD`*gdy' $dha$gd%g9:9<999999:::&:(:D:H:L:N:P:R:\:^:n:p::볢xeQQeQQ@!hQCJOJPJQJ^JaJo('h+)hCJOJPJQJ^JaJo($h+)hCJOJPJQJ^JaJ*hh5CJOJPJQJ^JaJo('hh5CJOJPJQJ^JaJ!hCJOJPJQJ^JaJo(!hy'CJOJPJQJ^JaJo(*huhhy'5CJOJPJQJ^JaJo(!h%gCJOJPJQJ^JaJo('hy'hy'CJOJPJQJ^JaJo(9999:N:::::::::::::::::$a$&`#$ *dhWD`*gd $dhG$a$gd *dhWD`*gdy' $dha$gd%g::::::::::::::::::::::::;jh}qU*htShtSmHnHsHuh}qjh}qUh; h;0Jjh;Uh(zjh(zU'hy'hy'CJOJPJQJ^JaJo(!h-CJOJPJQJ^JaJo(:; *dhWD`*gd6182P:p:7. A!"#$%SS *s066666668&6FVfv6888&6FVfv&6FVfv&6FVfv&6FVfv&6FVfv&6FVfv8XV~ 0@ 0@ 0@ 0@ 0@ 0@ 0@ 0@ 0@ 0@ 0@ 0@ 0@ 0@PJ_HmH nHsH tHF`F cke $1$a$CJKH_HmH nHsH tHdd +)h 1$dd1$@&[$\$a$&5CJ0KH$OJQJ\aJ0mHsHtH$A`$ ؞k=W[SONiN nfh*B*`Jph6V 6 +)Ǐvc>*B* `J ph6/6 +) ckee,g)ۏ CharCJKH\B\ !+)ckee,g $dd1$[$\$a$ CJKHOJQJaJmHsHtH>/> +) ckee,g CharCJOJQJ^JaJ4/!4 +)0u Char1 CJKHaJ8/18 +) yblFhe,g Char CJKHaJZRBZ %+)ckee,g)ۏ 2$dWD`CJOJ\aJmHsHtHF/QF $+) ckee,g)ۏ 2 CharCJKHOJ\aJ2/a2 +)u w Char CJKHaJ2r2 +);Ncke'WD`^J44 +);NckeN(WDZ`^JLL +)B~h)dWD`5CJ\^JPK![Content_Types].xmlN0EH-J@%ǎǢ|ș$زULTB l,3;rØJB+$G]7O٭V&Ŝ]6ҨN=Ina7qb&>!"h [+Lxz)WVOg%Ţ|8Mă#/8'=QU*C`CW{D6/[YL%+n+{\osM/~iBcAX/=x E'5&\h4da,yE\})laR^*zyV-WoWZN]:mV=tCWrb*IVURU|nc`|*^PK! ѐ'theme/theme/_rels/themeManager.xml.relsM 0wooӺ&݈Э5 6?$Q ,.aic21h:qm@RN;d`o7gK(M&$R(.1r'JЊT8V"AȻHu}|$b{P8g/]QAsم(#L[PK-![Content_Types].xmlPK-!֧6 0_rels/.relsPK-!kytheme/theme/themeManager.xmlPK-!ftheme/theme/theme1.xmlPK-! ѐ' theme/theme/_rels/themeManager.xml.relsPK] wL 3336>  .,Z-9:;  "$ LF,L19:;!#% -/6!!@ @H 0(  0(  B S  ? _Toc317229404 _Toc317230556 _Toc317232150 _Toc317361418 _Toc317618386 _Toc320816018 _Toc321140971 _Toc321208845 _Toc321522007 _Toc321556705x x-4?EVYZ`  "&(9@CLOX[\|"%&BJLOWXkvw69=>"=@AOR_`78DEcfmn  !$%EH]^-.89ORWZ[z{!%/0DJZ\lswz{  & * 7 8 d e  9 < I L N P Q S \ _ l n q + 0 6 9 ` c ~    5 8 H M U X / 4 > A  Z],/03<?X]bfy    "%&,-./0245<BDEGHJKMNux |{~.2e h F I e k P Q '+BDEGHJKMNux3s3ss333s3sss33s)?-|6< 7 BDEGHJKMNux44^`o(4~&jE8bA }. K N[ &*"y'+)s)-W0);2'6dj6:7W9R:_a=f=QP@:AffB=CZJ.KILKLaMYOzPPZQ9Q-RtSQTaTjY0[ ?]!a/fuhqNnl2r uFy[z98g@B|Fkr;AxJF la/tXz>^ "H>*H ju:}q%g0# 4}6WSXAW"B C2FvQ_G;M&gi9 tYp'6YBD@||||w,Unknown G.[x Times New Roman5Symbol3. .[x Arial;([SOSimSun-= |8N[A5  N[_GB2312N[;= |8ўSOSimHei?= .Cx Courier NewA$BCambria Math Qhc‚'*F m m !Z&!),.:;?]}    & 6"0000 0 0 00000 =@\]^([{  0 0 00000;[i::JQX) ?>2!xx`; u-N;Sf[b2010t^NGS,gbuՋNN~TՋ'Y~_o(u7b Administrator Oh+'0 ,8 X d p |4ҽѧԺ2010ררҵۺϿԴ ΢û Normal.dotmAdministrator7Microsoft Office Word@d@7e@zʠ@Zf m  ՜.+,D՜.+, X`t|  ΢й: d ?GKSOProductBuildVer2052-10.1.0.7023  !"#$%&()*+,-./0123456789:;<=>?@BCDEFGHJKLMNOPSTWRoot Entry F`r2V@1Table' 3WordDocument 8LSummaryInformation(ADocumentSummaryInformation8IMsoDataStoreP( e/NVME1LY==2P( e/Item PropertiesUCompObj n   FMicrosoft Word 97-2003 ĵ MSWordDocWord.Document.89q